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Mycosis fungoides masquerading as cutaneous lupus erythematosus and associated with antiphospholipid syndrome

Identifieur interne : 001981 ( Main/Exploration ); précédent : 001980; suivant : 001982

Mycosis fungoides masquerading as cutaneous lupus erythematosus and associated with antiphospholipid syndrome

Auteurs : E. C. Veysey [Royaume-Uni] ; J. D. Wilkinson [Royaume-Uni]

Source :

RBID : ISTEX:D1F3FB7A92361C9F1C2AB898D77FF9859A9B1755

English descriptors

Abstract

We report a case of a 69‐year‐old woman with mycosis fungoides (MF), who presented with clinical and histological features of cutaneous lupus, and for 6 years was treated for this, until repeated biopsies and gene‐rearrangement studies confirmed a diagnosis of MF. In addition, she developed thromboemboli and was found to have lupus anticoagulant antibodies. The possible biological relationship between antiphospholipid antibody syndrome and MF is considered. To our knowledge, this is the first reported case of MF masquerading as cutaneous lupus.

Url:
DOI: 10.1111/j.1365-2230.2007.02546.x


Affiliations:


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<term>Antiphospholipid antibodies</term>
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<term>Antiphospholipid syndrome</term>
<term>Atrophic epidermis</term>
<term>Basal liquefaction</term>
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<term>Cutaneous</term>
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<term>Erythematous</term>
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<term>Extensive involvement</term>
<term>Follicular</term>
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<div type="abstract" xml:lang="en">We report a case of a 69‐year‐old woman with mycosis fungoides (MF), who presented with clinical and histological features of cutaneous lupus, and for 6 years was treated for this, until repeated biopsies and gene‐rearrangement studies confirmed a diagnosis of MF. In addition, she developed thromboemboli and was found to have lupus anticoagulant antibodies. The possible biological relationship between antiphospholipid antibody syndrome and MF is considered. To our knowledge, this is the first reported case of MF masquerading as cutaneous lupus.</div>
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